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KMID : 0384119910110030545
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Korean Journal of Clinical Pathology
1991 Volume.11 No. 3 p.545 ~ p.548
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X-linked Agammaglobulinemia
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D. S. Kim
M. Y. Yoon/H. S. Lee
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Abstract
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X-kinked agammaglobulinemia is the most common type of primary immunodeficiency disorder. The disease is a sex linked recessive disorder carried by a gene on the long arm of the X-chromosome. It is characterized by serious pyogenic infections and marked diminution or absence of serum immunoglobulins of all classes. And those patients have virtually no circulating B lymphocytes. We experienced 7-year-old male and 26 month-year-old male patients(brothers) who complained of pus discharge on the lobe of left ear and fever. The patients showed marked panhypogammaglobulinemia and absence of circulating B lymphocytes at the immunologic
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